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Adult CF: Lung Health
If you have cystic fibrosis (CF), you need to work closely with your healthcare team. It will help you stay healthier, feel better, and have a better quality of life. It will also slow the decline in your lung function. Your care team may suggest many ways to maintain lung health. These may involve airway clearance therapy (ACT), medicine, nutrition, and exercise.
Airway clearance therapy
ACT helps loosen and clear mucus from your airways, letting you breathe better. It may also lower your risk for infection. There are several different ways to do ACT. Work with your healthcare provider to figure out the best one for you.
ACT often includes certain breathing and coughing techniques. You may also use a special device to loosen mucus. You may wear a vibrating vest. Or you may use a device called the flutter. It causes mucus in the airway to vibrate or flutter when you breathe through it.
You may also do chest physical therapy (CPT) to help loosen and clear thick secretions from the lungs. CPT greatly improves lung function. It also lowers the amount of lung damage over time. You will work with a physical therapist to learn how to do CPT. CPT often involves 3 techniques:
Postural drainage. Placing your body in certain positions can allow mucus to drain.
Percussion. Clapping or pounding on your chest and back may help loosen mucus. You may also use an airway clearance device, such as a vibrating vest, to do this technique.
Coughing. This simple technique can also help remove lung secretions.
You may need medicine to prevent or treat lung problems. Many of these are taken with a nebulizer. This device turns medicine into a mist so you can breathe it in. You may need to take:
Oral, inhaled, or IV (intravenous) antibiotics to prevent or treat lung infections
Bronchodilators (via a nebulizer or inhaler) to help open airways
Anti-inflammatory medicines to lessen airway inflammation
Medicines such as dornase alpha or hypertonic saline to thin secretions
Improving your nutrition can also help with your lung health. It can limit infections and help with other problems linked to CF. You may work with your care team to:
Change your diet by adding extra calories, salts, and fluids.
Eat more foods high in antioxidants. These are chemicals that reduce damage from inflammation in the body.
Take pancreatic enzymes to help you absorb nutrients.
Take vitamin supplements to replace those you don’t absorb from food.
Exercise helps you stay healthier. It improves your overall condition and helps you feel better. It also helps to loosen mucus, which makes it easier to breathe.
You should see a healthcare provider who is trained in treating CF every 3 months. If you have a cold or a breathing problem, you may need to see this healthcare provider more often. You can see your regular healthcare provider for minor problems not linked to CF.
When to call your healthcare provider
Call your healthcare provider right away if you have any of these:
Increased cough or amount of sputum
Wheezing or shortness of breath
Fever of 100.4°F (38°C) or higher, or as directed by your healthcare provider
Chest pain or tightness
Online Medical Reviewer:
Allen J Blaivas, DO
Online Medical Reviewer:
Daphne Pierce-Smith, RN, MSN, CCRC
Date Last Reviewed:
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